Saturday, November 10, 2012

Kidney Transplantation: Has it a role in patients with paraproteniemic renal disease?

There is a nice recent review of the role of kidney transplantation in patients with paraproteniemic renal disease (or plasma cell dyscrasia kidney disease or PCD) from the UK published in Nephron Clinical Practice - available open access.

“For patients with PCD it has generally been judged that transplantation is unlikely to be of benefit. Disease recurrence affecting the renal allograft, increased infection susceptibility and poor prognosis have been major concerns in these patients, limiting this treatment to anecdotal reports of highly selected cases. However, major improvements in the overall and progression-free survival due to newer treatment options, lead us to challenge the perception that patients with PCD are never suitable candidates for renal transplantation. As sustained periods of disease stabilization are currently possible, we suggest that renal transplantation may now be considered early in the course of the disease, especially in dialysis-dependent younger patients with a good performance status. In such patients, waiting for 3–5 years of sustained disease control to elapse appropriate before renal transplantation is not appropriate if the benefits of renal transplantation are to be maximized.”

Other key quotes from the article are:

Multiple Myeloma and Cast Nephropathy: “There are a number of isolated reports describing renal transplantation in patients with cast nephropathy coming from specialized centres. European Best Practice Guidelines [Nephrol Dial Transplant 2000;15(suppl 7)], advise a waiting period of at least 2 years between successful induction treatment and renal transplantation. However, with the availability of newer and more potent drugs, ASCT and novel treatment regimens, it is reasonable to reappraise these recommendations.”

Monoclonal Immunoglobulin Deposition Disease (MIDD): “Renal transplantation is generally not considered in patients with MIDD due to almost universal recurrence of the disease and poor survival of the allograft, though a small number of transplants have been performed with the possibility of prolonging patient survival. Early recurrence in the allograft is more common in MIDD patients in whom necrotizing or crescentic glomerulonephritis or membranoproliferative glomerulonephritis is a primary presentation of PCD in native kidneys.”

AL Amyloidosis: "Early experiences with renal transplantation in amyloidosis showed poor outcome with high post-transplant mortality and graft loss …In two of the biggest series so far. These studies have shown a renal allograft survival ranging from 18 to 72 months without clinical or histological evidence of recurrence. These data suggest that renal transplantation could be considered in patients with preserved performance status, who have little or no clinically significant amyloid deposition in other organs and have at least achieved a partial remission with chemotherapy with or without ASCT…..there is no clear guidance regarding renal transplantation in AL amyloidosis in current European Best Practice Guidelines [Nephrol Dial Transplant 2000;15(suppl 7)], it has not been considered as an absolute contraindication."